branching enzyme मीनिंग इन हिंदी

उदाहरण वाक्य

1. GBED is caused by an autosomal recessive mutation to the GBE1 gene, which leads glycogen branching enzyme activity that is reduced to absent.
2. Horses that are heterozygous for the GBED allele have been shown to have glycogen branching enzyme activity levels that were half that of an unaffected horse.
3. The branching enzyme can act upon only a branch having at least 11 residues, and the enzyme may transfer to the same glucose chain or adjacent glucose chains.
4. There are currently 3 subcategories of glycogen storage diseases in horses : Type 1 Polysaccharide Storage Myopathy, Glycogen Branching Enzyme Deficiency ( GBED ), and Type 2 Polysaccharide Storage Myopathy.
5. Specifically in this breed, complex rearrangements of glycogen branching enzyme ( GBE1 ) can cause a perinatal hypoglycaemic collapse and a late-juvenile-onset neuromuscular degeneration in glycogen storage disease type IV.
6. The glycogen branching enzyme catalyzes the transfer of a terminal fragment of six or seven glucose residues from a nonreducing end to the C-6 hydroxyl group of a glucose residue deeper into the interior of the glycogen molecule.
7. Glycoside hydrolase family 57 CAZY GH _ 57 comprises enzymes with several known activities; alpha-amylase ( ), 4-alpha-glucanotransferase ( ), ?-galactosidase ( ); amylopullulanase ( ); branching enzyme ( ).
8. Due to the heavy influx of American Quarter Horse breeding, some Paints may also carry genetic disorders such as Hyperkalemic Periodic Paralysis ( HYPP ), Hereditary Equine Regional Dermal Asthenia ( HERDA ), Equine polysaccharide storage myopathy ( called PSSM-polysaccharide storage myopathy-in Paints, Quarter Horses and Appaloosas ), Malignant hyperthermia ( MH ) and Glycogen Branching Enzyme Deficiency ( GBED ).